Nerve Ultrasound Studies in Poems Syndrome

2021 ◽  
Author(s):  
Qingyun Ding ◽  
Jian Li ◽  
Yuzhou Guan ◽  
Shuang Wu ◽  
Jingwen Niu ◽  
...  
Keyword(s):  
Poems Syndrome ◽  
Nerve Ultrasound ◽  
Ultrasound Studies

scholarly journals High-Resolution Nerve Ultrasound Abnormalities in POEMS Syndrome—A Comparative Study

Diagnostics ◽  
2021 ◽  
Vol 11 (2) ◽  
pp. 264
Author(s):  
Marc Dörner ◽  
Mihai Ceanga ◽  
Frank Schreiber ◽  
Jan-Hendrik Stahl ◽  
Cornelius Kronlage ◽  
...  
Keyword(s):  
High Resolution ◽  
Poems Syndrome ◽  
Syndrome Patient ◽  
Nerve Ultrasound ◽  
Cross Sectional ◽  
Skin Changes ◽  
Future Studies ◽  
Important Differential Diagnosis ◽  
Immune Mediated ◽  
Nerve Enlargement

Background: High-resolution nerve ultrasound (HRUS) has been proven to be a valuable tool in the diagnosis of immune-mediated neuropathies, such as chronic inflammatory demyelinating polyradiculoneuropathy (CIDP). POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M-protein, skin changes) is an important differential diagnosis of CIDP. Until now, there have been no studies that could identify specific HRUS abnormalities in POEMS syndrome patients. Thus, the aim of this study was to assess possible changes and compare findings with CIDP patients. Methods: We retrospectively analyzed HRUS findings in three POEMS syndrome and ten CIDP patients by evaluating cross-sectional nerve area (CSA), echogenicity and additionally calculating ultrasound pattern scores (UPSA, UPSB, UPSC and UPSS) and homogeneity scores (HS). Results: CIDP patients showed greater CSA enlargement and higher UPSS (median 14 vs. 11), UPSA (median 11.5 vs. 8) and HS (median 5 vs. 3) compared with POEMS syndrome patients. However, every POEMS syndrome patient illustrated enlarged nerves exceeding reference values, which were not restricted to entrapment sites. In CIDP and POEMS syndrome, heterogeneous enlargement patterns could be identified, such as inhomogeneous, homogeneous and regional nerve enlargement. HRUS in CIDP patients visualized both increased and decreased echointensity, while POEMS syndrome patients pictured hypoechoic nerves with hyperechoic intraneural connective tissue. Discussion: This is the first study to demonstrate HRUS abnormalities in POEMS syndrome outside of common entrapment sites. Although nerve enlargement was more prominent in CIDP, POEMS syndrome patients revealed distinct echogenicity patterns, which might aid in its differentiation from CIDP. Future studies should consider HRUS and its possible role in determining diagnosis, prognosis and treatment response in POEMS syndrome.

POEMS Syndrome: Two Cases Report

1998 ◽  
Vol 39 (1) ◽  
pp. 169
Author(s):  
Eun Young Ko ◽  
Ik Yang ◽  
Kyung Won Lee ◽  
Yul Lee ◽  
Soo Young Chung ◽  
...  
Keyword(s):  
Poems Syndrome

A Case of Crow-Fukase (POEMS) Syndrome Presenting with Multiple Hemangioma and Edema of Legs

2006 ◽  
Vol 68 (4) ◽  
pp. 390-394
Author(s):  
Chiaki KUWABARA ◽  
Makoto INAOKI ◽  
Wataru FUJIMOTO ◽  
Hideho WADA ◽  
Yoshito SADAHIRA ◽  
...  
Keyword(s):  
Poems Syndrome

POEMS syndrome: atypical presentation and therapeutic consideration

2020 ◽  
pp. 65-69
Author(s):  
Ayman Abukamar ◽  
Majdi Abu-Awida ◽  
Saeed Abughazaleh ◽  
Ahmad Abdallah ◽  
Hamza Al-Zghool
Keyword(s):  
Poems Syndrome ◽  
Atypical Presentation ◽  
Therapeutic Consideration

Fascicular torsions of the anterior and posterior interosseous nerve in 4 cases: neuroimaging methods to improve diagnosis

2020 ◽  
Vol 132 (6) ◽  
pp. 1925-1929 ◽  
Author(s):  
Jennifer Kollmer ◽  
Paul Preisser ◽  
Martin Bendszus ◽  
Henrich Kele
Keyword(s):  
Magnetic Resonance ◽  
Surgical Intervention ◽  
Case Series ◽  
Diagnostic Methods ◽  
Posterior Interosseous Nerve ◽  
Nerve Ultrasound ◽  
Magnetic Resonance Neurography ◽  
Surgical Exploration ◽  
Hyperintense Signal ◽  
Emergency Surgical Intervention

Diagnosis of spontaneous fascicular nerve torsions is difficult and often delayed until surgical exploration is performed. This case series raises awareness of peripheral nerve torsions and will facilitate an earlier diagnosis by using nerve ultrasound (NUS) and magnetic resonance neurography (MRN). Four patients with previously ambiguous upper-extremity mononeuropathies underwent NUS and 3T MRN. Neuroimaging detected proximal torsions of the anterior and posterior interosseous nerve fascicles within median or radial nerve trunks in all patients. In NUS, most cases presented with a thickening of affected nerve fascicles, followed by an abrupt caliber decrease, leading to the pathognomonic sausage-like configuration. MRN showed T2-weighted hyperintense signal alterations of fascicles at and distal to the torsion site, and directly visualized the distorted nerves. Three patients had favorable outcomes after being transferred to emergency surgical intervention, while 1 patient with existing chronic muscle atrophy was no longer eligible for surgery. NUS and MRN are complementary diagnostic methods, and both can detect nerve torsions on a fascicular level. Neuroimaging is indispensable for diagnosing fascicular nerve torsions, and should be applied in all unclear cases of mononeuropathy to determine the diagnosis and if necessary, to guide surgical therapies, as only timely interventions enable favorable outcomes.

Intérêt de l'autogreffe de cellules souches hématopoïétiques dans le traitement du POEMS syndrome

2001 ◽  
Vol 22 ◽  
pp. 508s
Author(s):  
M. Soubrier ◽  
M. Ruivard ◽  
O. Aumaitre ◽  
B. Sauvezie ◽  
P. Philippe
Keyword(s):  
Poems Syndrome ◽  
Cellules Souches Hématopoïétiques
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