scholarly journals Langerhans Cell Histiocytosis Presenting With Late‐Onset Sporadic Ataxia

2019 ◽  
Vol 6 (8) ◽  
pp. 716-718
Author(s):  
Inder Puri ◽  
Divyani Garg ◽  
Achal Kumar Srivastava ◽  
Lavleen Singh ◽  
Garima Shukla ◽  
...  
Keyword(s):  
Langerhans Cell Histiocytosis ◽  
Late Onset ◽  
Langerhans Cell ◽  
Sporadic Ataxia

Acral, Pure Cutaneous, Self-Healing, Late-Onset, Cellulitis-Like Langerhans Cell Histiocytosis

2009 ◽  
Vol 13 (1) ◽  
pp. 43-47
Author(s):  
Prafulla Kumar Sharma ◽  
Sunil Sabhnani ◽  
Minakshi Bhardwaj ◽  
Hemanta Kumar Kar
Keyword(s):  
Langerhans Cell Histiocytosis ◽  
Clinical Presentation ◽  
Late Onset ◽  
Early Adulthood ◽  
Langerhans Cell ◽  
Self Healing ◽  
Diagnostic Dilemma

Background: An unusual and not yet reported clinical presentation of pure cutaneous Langerhans cell histiocytosis (LCH) that was a diagnostic dilemma. Objective: To bring to light the newer presentation of this disease. Method: The case was managed on clinical grounds initially as cellulitis. However, after the investigations and confirmation of the diagnosis, she was managed symptomatically. Results: Pure cutaneous LCH may manifest in early adulthood with features of cellulitis, erythematous edematous vesicular plaques, and nodules distributed in the flexural acral areas. Conclusion: Pure cutaneous LCH may have an acute late onset with unusual morphology as cellulitis, inverse acral distribution, and self-healing.

Late-onset self-healing reticulohistiocytosis: Pediatric case of Hashimoto?Pritzker type Langerhans cell histiocytosis

2007 ◽  
Vol 34 (3) ◽  
pp. 205-209 ◽  
Author(s):  
Kyoko NAKAHIGASHI ◽  
Miyuki OHTA ◽  
Rie SAKAI ◽  
Yasushi SUGIMOTO ◽  
Yukiko IKOMA ◽  
...  
Keyword(s):  
Langerhans Cell Histiocytosis ◽  
Late Onset ◽  
Langerhans Cell ◽  
Self Healing ◽  
Pediatric Case

Late-onset self-healing Langerhans cell histiocytosis in a patient with atopic dermatitis

2014 ◽  
Vol 41 (5) ◽  
pp. 450-451 ◽  
Author(s):  
Takeshi Nakahara ◽  
Makiko Kido-Nakahara ◽  
Eriko Itoh ◽  
Masutaka Furue
Keyword(s):  
Atopic Dermatitis ◽  
Langerhans Cell Histiocytosis ◽  
Late Onset ◽  
Langerhans Cell ◽  
Self Healing

scholarly journals Late‐onset Langerhans cell histiocytosis without extracutaneous involvement

2020 ◽  
Vol 3 (4) ◽  
pp. 94-95
Author(s):  
Mai Iwata ◽  
Takuya Takeichi ◽  
Yoshinao Muro ◽  
Masashi Akiyama
Keyword(s):  
Langerhans Cell Histiocytosis ◽  
Late Onset ◽  
Langerhans Cell

scholarly journals Late-Onset Langerhans Cell Histiocytosis with Cerebellar Ataxia as an Initial Symptom

2016 ◽  
Vol 8 (3) ◽  
pp. 218-223 ◽  
Author(s):  
Jung-Min Pyun ◽  
Hyeyoung Park ◽  
Kyung Chul Moon ◽  
Beomseok Jeon
Keyword(s):  
White Matter ◽  
Diabetes Insipidus ◽  
Medical History ◽  
Cerebellar Ataxia ◽  
Langerhans Cell Histiocytosis ◽  
Late Onset ◽  
Langerhans Cell ◽  
Systemic Review ◽  
Initial Symptom ◽  
Secondary Causes

Late-onset progressive cerebellar ataxia is a diagnostic challenge because of a poor correlation between genotype and phenotype, and a broad range of secondary causes that extend beyond the neurological field. We report the case of a 45-year-old woman admitted after 2 years of slowly progressing cerebellar ataxia, dysarthria, and emotional instability. Notably, she was diagnosed with diabetes insipidus at the age of 35. As ‘idiopathic cerebellar ataxia’ was suspected, diagnostic tests, including genetic testing as well as serum and cerebrospinal fluid analyses, and brain magnetic resonance imaging (MRI) were performed. All results were normal except those of MRI, performed 9 months prior to admission, which showed multiple dot-like white matter lesions with unclear cause. On a repeated brain MRI, a new lesion presenting as a 1.5-cm-sized highly enhancing mass attached to the right frontal skull was found. A sharply marginated lytic skull defect was also evident on skull X-ray, which corresponded to the lesion mass. Given these new radiological findings, a systemic review of the patient’s medical history for rare secondary causes of cerebellar ataxia was performed, with particular attention to her past ‘diabetes insipidus’. The mass, lytic lesion of the skull, white matter lesion, diabetes insipidus, and cerebellar ataxia all suggested a final diagnosis of Langerhans cell histiocytosis (LCH), which was confirmed histopathologically. This is a rare case of late-onset LCH with an unusual initial symptom which underlines the importance of carefully reviewing the patient’s medical history and broadening the search for etiologies beyond the nervous system.

scholarly journals Solitary, Late-onset, Self-healing Langerhans Cell Histiocytosis

2011 ◽  
Vol 91 (1) ◽  
pp. 103-104 ◽  
Author(s):  
S Murata ◽  
Y Yoshida ◽  
K Adachi ◽  
E Morita ◽  
O Yamamoto
Keyword(s):  
Langerhans Cell Histiocytosis ◽  
Late Onset ◽  
Langerhans Cell ◽  
Self Healing

Langerhans cell histiocytosis and thyroid carcinoma

1998 ◽  
Vol 138 (5) ◽  
pp. 909-910 ◽  
Author(s):  
Marzano ◽  
Gasparini ◽  
Grammatica ◽  
De Juli ◽  
Caputo
Keyword(s):  
Thyroid Carcinoma ◽  
Langerhans Cell Histiocytosis ◽  
Langerhans Cell

Cytogenetic abnormalities in PHA-stimulated lymphocytes from patients with Langerhans cell histiocytosis

2000 ◽  
Vol 111 (1) ◽  
pp. 258-262 ◽  
Author(s):  
Susi Scappaticci ◽  
Cesare Danesino ◽  
Elena Rossi ◽  
Catherine Klersy ◽  
Gian Mario Fiori ◽  
...  
Keyword(s):  
Langerhans Cell Histiocytosis ◽  
Langerhans Cell ◽  
Cytogenetic Abnormalities
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