Extensive Multifocal Rosai-Dorfman Disease Involving the Central Nervous System and Paranasal Sinuses

2011 ◽  
Vol 121 (S4) ◽  
pp. S234-S234 ◽  
Author(s):  
Grace G. Kim ◽  
Marc E. Friedel ◽  
Jean Anderson Eloy ◽  
Robert W. Jyung ◽  
James K. Liu
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Paranasal Sinuses ◽  
Rosai Dorfman Disease ◽  
The Central Nervous System

Rosai-Dorfman disease involving the central nervous system: seven cases from one institute

2015 ◽  
Vol 157 (9) ◽  
pp. 1565-1571 ◽  
Author(s):  
Yongji Tian ◽  
Junmei Wang ◽  
Mingtao Li ◽  
Song Lin ◽  
Guihuai Wang ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Rosai Dorfman Disease ◽  
The Central Nervous System

Regression of intracranial Rosai–Dorfman disease following corticosteroid therapy

2006 ◽  
Vol 104 (5) ◽  
pp. 840-844 ◽  
Author(s):  
Christopher M. McPherson ◽  
Justin Brown ◽  
Angela W. Kim ◽  
Franco Demonte
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Corticosteroid Therapy ◽  
Histopathological Analysis ◽  
Extranodal Involvement ◽  
First Case ◽  
Rosai Dorfman Disease ◽  
Effective Option ◽  
The Central Nervous System ◽  
Skull Base Lesions

✓ Rosai–Dorfman disease (RDD) is an idiopathic histioproliferative disorder usually presenting with massive, painless lymphadenopathy. Extranodal involvement has been reported including at least 50 cases affecting the central nervous system (CNS). The treatment of CNS RDD as reported in the literature has primarily involved a surgical technique. The authors report on the case of a 53-year-old man presenting with multiple skull base lesions mimicking meningiomas. The patient suffered visual deterioration and underwent a right orbitopterional craniotomy as well as optic nerve decompression. Histopathological analysis revealed histiocytic cells and emperipolesis consistent with RDD. Following surgery, corticosteroid agents were administered, leading to marked resolution of both the remaining surgically untreated lesions and the balance of the patient's symptoms. This report represents the first case of the resolution of intracranial RDD following corticosteroid therapy. Corticosteroid agents should be considered an effective option in the treatment of CNS RDD.

scholarly journals Rosai-Dorfman Disease of the Central Nervous System

Medicine ◽  
2014 ◽  
Vol 93 (3) ◽  
pp. 165-175 ◽  
Author(s):  
Jose D. Sandoval-Sus ◽  
Ana C. Sandoval-Leon ◽  
Jennifer R. Chapman ◽  
Jose Velazquez-Vega ◽  
Maria J. Borja ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Rosai Dorfman Disease ◽  
The Central Nervous System

scholarly journals Meninges Outside the Meninges: Ectopic Meningiomas and Meningothlelial Proliferations

2021 ◽  
Author(s):  
John A. Ozolek
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Parotid Gland ◽  
Nasal Cavity ◽  
Head And Neck ◽  
Paranasal Sinuses ◽  
Clinicopathological Features ◽  
Anatomical Region ◽  
The Central Nervous System

Extracranial meningiomas have been reported for decades now and have been described in the head and neck; calvarial, nasal cavity, paranasal sinuses, nasopharynx, parotid gland and in various remote anatomical locations systemically. The presence of microanatomical structures for all intents and purposes resembling and having the histopathological characteristics of meninges outside of the central nervous system meninges is uncommon but well-documented. Typically, these lesions are found in the lung or part of hamartomatous/choristomatous lesions and frequently occur in the head and neck anatomical region. The lesion first described by Suster and Rosai termed \"hamartoma of the scalp with ectopic meningothelial elements\" is the prototypical example of lesions with meningothelial elements. We have described recently a similar hamartomatous lesion with meningothelial elements occurring in the tongue. In this chapter, we will review the clinicopathological features of ectopic meningiomas and lesions that contain meningothelial elements and their possible pathogenesis.

scholarly journals Pearls & Oy-sters: Rosai-Dorfman Disease of the Central Nervous System

Neurology ◽  
2021 ◽  
pp. 10.1212/WNL.0000000000012035
Author(s):  
Kia Gilani ◽  
Stephanie Kuntz ◽  
David G. Munoz ◽  
Raphael Schneider
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Rosai Dorfman Disease ◽  
The Central Nervous System

scholarly journals Radiological and clinical findings of isolated meningeal Rosai–Dorfman disease of the central nervous system

Medicine ◽  
2019 ◽  
Vol 98 (19) ◽  
pp. e15365 ◽  
Author(s):  
Jia-Hua Wen ◽  
Chao Wang ◽  
Yun-Yun Jin ◽  
Duo Xu ◽  
Biao Jiang ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Clinical Findings ◽  
Rosai Dorfman Disease ◽  
The Central Nervous System
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