scholarly journals Cardiac MRI evaluation of hypertrophic cardiomyopathy: Left ventricular outflow tract/aortic valve diameter ratio predicts severity of LVOT obstruction

2012 ◽  
Vol 36 (3) ◽  
pp. 598-603 ◽  
Author(s):  
Jens Vogel-Claussen ◽  
Miguel Santaularia Tomas ◽  
Amit Newatia ◽  
Danielle Boyce ◽  
Aurelio Pinheiro ◽  
...  
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Aortic Valve ◽  
Cardiac Mri ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Diameter Ratio ◽  
Left Ventricular Outflow ◽  
Mri Evaluation ◽  
Aortic Valve Diameter

scholarly journals Totally Endoscopic Septal Myectomy in a Patient with Aortic Prothesis and Complicated with Lymphoma

2020 ◽  
Author(s):  
Huimin Cui ◽  
Lin Zhang ◽  
Shixiong Wei ◽  
Shengli Jiang
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Aortic Valve ◽  
Left Ventricular Outflow Tract ◽  
Standard Procedure ◽  
Median Sternotomy ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Current Standard ◽  
Septal Myectomy ◽  
Left Ventricular Outflow

Abstract The Morrow procedure which uses a median sternotomy with the left ventricle and septum accessed by the aortic valve through a vertical aortotomy is the current standard procedure for left ventricular outflow tract obstruction in hypertrophic cardiomyopathy. However, this approach may be limited in patients who have previously undergone aortic valve replacement. Here, we present a patient who complicated with lymphoma underwent endoscopic septal myectomy to preserve the previously implanted aortic prosthesis. Keywords: Endoscopic surgery, hypertrophic cardiomyopathy, septal myectomy.

scholarly journals Cardiac amyloidosis: The great masquerader

2018 ◽  
Vol 2018 (2) ◽  
Author(s):  
Jubran Rind ◽  
Nagib Chalfoun ◽  
Richard McNamara
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Cardiac Mri ◽  
Cardiac Amyloidosis ◽  
Ventricular Hypertrophy ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Asymmetric Septal Hypertrophy ◽  
Left Ventricular Outflow ◽  
Septal Hypertrophy

Cardiac amyloidosis is an elusive condition that is notorious for mimicking various cardiovascular conditions that present with left ventricular hypertrophy (LVH). The hypertrophy in amyloidosis is typically diffuse; however, rare reports of echocardiographic resemblances with hypertrophic cardiomyopathy (HCM) exist, such as asymmetric septal hypertrophy and left ventricular outflow tract obstruction. Cardiac MRI can help differentiate amyloidosis from hypertrophic cardiomyopathy in unclear situations. This differentiation from HCM and other forms of cardiomyopathy has important treatment implications. Here we present the case of a 76-year-old man with cardiomyopathy who had echocardiographic features of asymmetric hypertrophic cardiomyopathy but was correctly diagnosed with amyloidosis with the help of cardiac MRI and ECG.

Abstract 3261: Papillary Fibroelastomas in Hypertrophic Cardiomyopathy

Circulation ◽  
2007 ◽  
Vol 116 (suppl_16) ◽  
Author(s):  
Gautam Kumar ◽  
Ryan J MacDonald ◽  
Paul Sorajja ◽  
William D Edwards ◽  
Steve R Ommen ◽  
...  
Keyword(s):  
Risk Factor ◽  
Hypertrophic Cardiomyopathy ◽  
Aortic Valve ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Outflow Tract ◽  
Cardiac Tumors ◽  
Left Ventricular Outflow ◽  
Heart Lesions

Introduction: Papillary fibroelastomas (PFEs) are the 3rd most common primary cardiac tumors with a prevalence of around 0.01% in patients with echocardiograms. The pathogenesis is controversial but endocardial trauma has been implicated. We hypothesized that increased turbulence in hypertrophic cardiomyopathy (HCM) would be a risk factor for PFE development and characterized PFEs in HCM. Around 5% of HCM patients had neurologic events. We postulated that patients with both PFE and HCM had a higher risk of neurologic events. Methods: We reviewed pathology records from 1990 –2006 and identified 129 subjects with PFEs and 2479 patients with HCM. We then identified the subjects who had both HCM and PFE (n = 19). All subjects signed release for use of their medical records for research. Results: 19 subjects (68.4% female) had both HCM and PFE. Mean age at diagnosis of HCM was 49 (range 21– 81) years. All had outflow tract obstruction with resting gradient >/=30 mm Hg except 2 who had resting gradients <30 mm Hg but elevated gradients on provocation. PFE diagnosis was after a mean of 9.7 years (SD 8.3) following HCM diagnosis. 5 subjects were diagnosed pre-operatively by transthoracic echocardiography, 2 subjects by transesophageal echocardiography and 12 subjects at surgery only. Most subjects had only 1 PFE (57.9%) but 1 subject had as many as 40 tumors. Most PFEs were on the aortic valve (47.4%) and the left ventricular side of the septum and left ventricular outflow tract (42.1%). Only 2 patients had right heart lesions that were presumably unrelated to HCM. 3 patients had previous septal myectomies and all 3 had PFEs near the previous resection. 5 of 19 subjects (26.3%) with PFE and HCM had neurologic events (either strokes or transient ischemic attacks) compared to 199 of 2261 subjects (8.8%) with HCM alone (OR = 4.1; 95% CI 1.4 –11.4, p < 0.05). Conclusion: Nearly 90% of PFEs in HCM are located in the septum, left ventricular outflow tract and aortic valve. This may be supportive of endocardial trauma as a risk factor for PFE development in HCM. About a quarter of patients with PFEs and HCM had neurologic events. This may indicate that these lesions are not innocuous and should perhaps be actively searched for in patients with HCM and unexplained neurologic events.

Angina Pectoris Due to Severe Muscular Bridge in Hypertrophic Cardiomyopathy

1998 ◽  
Vol 6 (2) ◽  
pp. 132-134
Author(s):  
M Şah Topcuoĝlu ◽  
Ayhan Usal ◽  
Cem Kayhan ◽  
Aladdin Pekedis ◽  
Acar Tokcan ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Calcium Antagonist ◽  
Hypertrophic Cardiomyopathy ◽  
Angina Pectoris ◽  
Left Ventricular Outflow Tract ◽  
Young Patients ◽  
Ventricular Outflow Tract ◽  
Myocardial Scintigraphy ◽  
Left Ventricular ◽  
Left Ventricular Outflow

We report the case of a 39-year-old male with hypertrophic cardiomyopathy who complained of angina pectoris. The patient was treated with a beta blocker and a calcium antagonist without effect. Myocardial scintigraphy revealed anterior ischemia. Cardiac catheterization and ventriculography revealed severe systolic narrowing of the left anterior descending coronary artery and no significant pressure gradient across the left ventricular outflow tract. Myotomy was performed on a muscular bridge over the left anterior descending coronary artery and the patient's angina was relieved. In young patients with hypertrophic cardiomyopathy who develop angina refractory to medical therapy, a coexisting muscular bridge should be sought.

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