scholarly journals Non-Val30Met mutation, septal hypertrophy, and cardiac denervation in patients with mutant transthyretin amyloidosis

2018 ◽  
Vol 6 (1) ◽  
pp. 122-130 ◽  
Author(s):  
Kyoko Hirakawa ◽  
Seiji Takashio ◽  
Kyohei Marume ◽  
Masahiro Yamamoto ◽  
Shinsuke Hanatani ◽  
...  
Keyword(s):  
Transthyretin Amyloidosis ◽  
Cardiac Denervation ◽  
Septal Hypertrophy

Modified Septal Myectomy Using a Curved Knife for Left Ventricular Septal Hypertrophy

2014 ◽  
Vol 17 (5) ◽  
pp. 269
Author(s):  
Shinya Takahashi ◽  
Taiichi Takasaki ◽  
Futoshi Tadehara ◽  
Takahiro Taguchi ◽  
Keijiro Katayama ◽  
...  
Keyword(s):  
Blood Flow ◽  
Chest Pain ◽  
Aortic Valve ◽  
Cross Section ◽  
Left Ventricular ◽  
Chest Discomfort ◽  
Septal Myectomy ◽  
Asymmetric Septal Hypertrophy ◽  
Septal Hypertrophy ◽  
Septal Myocardium

An 86-year-old woman presented with chest pain and discomfort. Echocardiography revealed severe aortic valve stenosis and asymmetric septal hypertrophy. Aortic valve replacement and myectomy were performed using a curved knife. The blade was U-shaped in cross-section, and was curved upward along the long axis. Hypertrophic septal myocardium was removed along the long axis of the left ventricle (LV), and a groove for blood flow was constructed. The patient was discharged uneventfully without recurrence of her chest discomfort. Our result suggested that a curved knife is a reasonable option for transaortic septal myectomy in patients with obstructive LV hypertrophy.

A Combination of Pharmacophore and In silico Approaches for Identification of Potential Transthyretin Amyloidosis Inhibitors

2014 ◽  
Vol 11 (3) ◽  
pp. 339-348
Author(s):  
Zheng-Li Zhou ◽  
Hsuan-Liang Liu ◽  
Josephine Wu ◽  
Cheng-Wen Tsao ◽  
Wei-Hsi Chen ◽  
...  
Keyword(s):  
In Silico ◽  
Transthyretin Amyloidosis

Effects of Cardiac Denervation on Development of Heart Failure and Catecholamine Desensitization

Circulation ◽  
1997 ◽  
Vol 95 (8) ◽  
pp. 2130-2140 ◽  
Author(s):  
Naoki Sato ◽  
Stephen F. Vatner ◽  
You-Tang Shen ◽  
Raymond K. Kudej ◽  
Bijan Ghaleh-Marzban ◽  
...  
Keyword(s):  
Heart Failure ◽  
Cardiac Denervation

scholarly journals Echocardiographic Findings in Friedreich's Ataxia

1976 ◽  
Vol 3 (4) ◽  
pp. 329-332 ◽  
Author(s):  
H.F. Gattiker ◽  
A. Davignon ◽  
A. Bozio ◽  
J. Batlle-Diaz ◽  
G. Geoffroy ◽  
...  
Keyword(s):  
Friedreich’S Ataxia ◽  
Left Ventricular ◽  
Friedreich's Ataxia ◽  
Ventricular Free Wall ◽  
Slight Reduction ◽  
Free Wall ◽  
Left Ventricular Free Wall ◽  
Echocardiographic Examination ◽  
Septal Hypertrophy ◽  
Echocardiographic Findings

SUMMARY:Echocardiographic examination of 21 patients with Friedreich's ataxia (age 7 to 28 years) showed cardiac abnormalities in 90% of the cases. They were characterized by varying degrees of septal hypertrophy in 81%, left ventricular free wall hypertrophy in 61%, and a slight reduction of left ventricular internal dimension in 57% of the cases. Asymmetric septal hypertrophy (ASH) with a septal/left ventricular free wall ratio of over 1.3 was found in 29% of the cases, and systolic anterior motion (SAM) of the mitral valve in three patients. Two other patients showed evidence of a different type of cardiomyopathy with marked symmetric left ventricular hypertrophy and marked left ventricular enlargement.

scholarly journals A Descriptive Analysis of ATTR Amyloidosis in Spain from the Transthyretin Amyloidosis Outcomes Survey

2021 ◽  
Author(s):  
Juan González-Moreno ◽  
Inés Losada-López ◽  
Eugenia Cisneros-Barroso ◽  
Pablo Garcia-Pavia ◽  
José González-Costello ◽  
...  
Keyword(s):  
Descriptive Analysis ◽  
Transthyretin Amyloidosis ◽  
Attr Amyloidosis

Characterization of population genetic structure of hereditary transthyretin amyloidosis in Bulgaria

Amyloid ◽  
2021 ◽  
pp. 1-7
Author(s):  
Zornitsa Pavlova ◽  
Stayko Sarafov ◽  
Tihomir Todorov ◽  
Andrey Kirov ◽  
Teodora Chamova ◽  
...  
Keyword(s):  
Genetic Structure ◽  
Population Genetic Structure ◽  
Population Genetic ◽  
Transthyretin Amyloidosis ◽  
Hereditary Transthyretin Amyloidosis
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