Extraosseous Ewing's sarcoma arising in the perineal region (Rectovaginal Septum)

2013 ◽  
Vol 42 (11) ◽  
pp. 1002-1005 ◽  
Author(s):  
Mitsuaki Ishida ◽  
Muneo Iwai ◽  
Keiko Yoshida ◽  
Akiko Kagotani ◽  
Hidetoshi Okabe
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Rectovaginal Septum ◽  
Perineal Region ◽  
Extraosseous Ewing’S Sarcoma

The First Report of Extraosseous Ewing's Sarcoma in the Rectovaginal Septum

2002 ◽  
Vol 88 (4) ◽  
pp. 345-346 ◽  
Author(s):  
Marija Petković ◽  
Gordana Zamolo ◽  
Damir Muhvić ◽  
Miran Čoklo ◽  
Sanja Štifter ◽  
...  
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Malignant Neoplasm ◽  
External Beam Radiation ◽  
X Rays ◽  
Rectovaginal Septum ◽  
Beam Radiation ◽  
Palpable Mass ◽  
Residual Mass ◽  
Extraosseous Ewing’S Sarcoma

Aims and Background To report an extremely rare case of Ewing's sarcoma located in the rectovaginal septum. Ewing's sarcoma is a highly malignant neoplasm of bone, which usually occurs during childhood. Common extraosseous localizations of Ewing's sarcoma include the trunk, extremities, uterus, cervix and vagina. Methods A 45-year-old woman presented to us with a six-month history of pain in the lower abdomen during intercourse. Pelvic examination was performed and a palpable mass was found. The mass had a size of 9 × 6 cm, a soft tissue consistency, was partially movable and the patient felt the pain during palpation. Examination of the inguinal lymph nodes revealed no signs of inguinal adenopathy. The results of laboratory tests, rectoscopy, chest X-rays, barium enema and bone scan were normal. Computed tomography (CT) showed an inhomogeneous expansive mass in the rectovaginal septum measuring 8.7 × 6.1 cm, without any signs of rectum or bladder invasion. The vascular structures of the pelvis were normal. At laparotomy the process was judged inoperable and only biopsy of the tumor mass was carried out. Histology showed a neoplasm with small, round to oval cells with scarce cytoplasm. Immunohistology with the monoclonal antibody CD99 (MIC-2 gene product, Ewing's sarcoma marker, clone 12E7, DAKO A/S, Glostrup, Denmark) revealed an extraosseous Ewing's sarcoma. The patient was treated with chemotherapy followed by whole-pelvis external beam radiation and intracavitary brachytherapy. Results A residual mass measuring 3.5 × 2.5 cm was visible on a control CT scan 18 months after treatment; however, the patient was feeling well and refused surgery to remove the residual mass. Conclusions To our knowledge this is the first reported case of extraosseous Ewing's sarcoma in the rectovaginal septum.

scholarly journals Extraosseous Ewing’s Sarcoma: Pictorial Review of Imaging Findings, Differential Diagnosis, and Pathologic Correlation

2021 ◽  
Author(s):  
Alan Alexander ◽  
Kyle Hunter ◽  
Michael Rubin ◽  
Ambarish P. Bhat
Keyword(s):  
Differential Diagnosis ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Multimodality Imaging ◽  
Imaging Features ◽  
Older Children ◽  
Radiologic Findings ◽  
Pictorial Review ◽  
Malignant Mesenchymal Tumor ◽  
Extraosseous Ewing’S Sarcoma

AbstractExtraosseous Ewing’s sarcoma (EES), first described in 1969, is a malignant mesenchymal tumor just like its intraosseous counterpart. Although Ewing’s sarcomas are common bone tumors in young children, EESs are rarer and more commonly found in older children/adults, often carrying a poorer prognosis. We discuss the multimodality imaging features of EES and the differential diagnosis of an aggressive appearing mass in proximity to skeletal structures, with pathologic correlates. This review highlights the need to recognize the variability of radiologic findings in EES such as the presence of hemorrhage, rich vascularity, and cystic or necrotic regions and its imaging similarity to other neoplasms that are closely related pathologically.

Pazopanib for recurrent extraosseous Ewing's sarcoma of the retroperitoneum

2014 ◽  
Vol 21 (11) ◽  
pp. 1183-1184 ◽  
Author(s):  
Yutaka Yamamoto ◽  
Masahiro Nozawa ◽  
Nobutaka Shimizu ◽  
Takafumi Minami ◽  
Kazuhiro Yoshimura ◽  
...  
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Extraosseous Ewing’S Sarcoma

Primary intracranial extraosseous Ewing’s sarcoma

2018 ◽  
Vol 35 (3) ◽  
pp. 541-545
Author(s):  
Amir Humza Sohail ◽  
Mohammed Sachal ◽  
Muhammad Arslan Arif Maan ◽  
Muhammad Soban ◽  
Muhammad Salman Khan ◽  
...  
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Extraosseous Ewing’S Sarcoma

scholarly journals Adult Primary Spinal Epidural Extraosseous Ewing’s Sarcoma: A Case Report and Review of the Literature

2016 ◽  
Vol 2016 ◽  
pp. 1-8 ◽  
Author(s):  
Mark Bustoros ◽  
Cheddhi Thomas ◽  
Joshua Frenster ◽  
Aram S. Modrek ◽  
N. Sumru Bayin ◽  
...  
Keyword(s):  
Epidural Space ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Gross Total Resection ◽  
Review Of The Literature ◽  
Total Resection ◽  
Improved Outcomes ◽  
Rare Malignancy ◽  
Extraosseous Ewing’S Sarcoma ◽  
Spinal Epidural

Background. Extraosseous Ewing’s sarcoma in the spinal epidural space is a rare malignancy, especially in adults.Case Presentation. A 40-year-old male presented with back pain and urinary hesitancy. MRI revealed a thoracic extradural mass with no osseous involvement. He underwent surgery for gross total resection of the mass, which was diagnosed as Ewing’s sarcoma. He was subsequently treated with chemoradiotherapy. He remains disease-free 1 year after surgery. Review of the literature indicated only 45 previously reported cases of spinal epidural extraosseous Ewing’s sarcoma in adults.Conclusions. Extraosseous Ewing’s sarcoma in the spinal epidural space is a rare clinical entity that should be included in the differential for spinal epidural masses. Its treatment is multidisciplinary but frequently requires surgical intervention due to compressive neurologic symptoms. Gross total resection appears to correlate with improved outcomes.

scholarly journals Spinal intradural extraosseous Ewing's sarcoma

Rare Tumors ◽  
2011 ◽  
Vol 3 (1) ◽  
pp. 21-24 ◽  
Author(s):  
Farrah J. Mateen ◽  
Aziza Nassar ◽  
Aditya Bardia ◽  
Aminah Jatoi ◽  
Michael G. Haddock ◽  
...  
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Extraosseous Ewing’S Sarcoma

scholarly journals Extraosseous Ewing's sarcoma of the maxillary sinus: A very rare entity

2018 ◽  
Vol 39 (3) ◽  
pp. 380 ◽  
Author(s):  
LakshmiKeerthana Killampalli ◽  
ARavi Prakash ◽  
AVikram Simha Reddy ◽  
M Rajinikanth
Keyword(s):  
Maxillary Sinus ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Rare Entity ◽  
Extraosseous Ewing’S Sarcoma
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