scholarly journals Thrombosed pulmonary arterial aneurysm in eisenmenger's syndrome

1999 ◽  
Vol 22 (2) ◽  
pp. 127-127 ◽  
Author(s):  
Edward A. Geiser ◽  
Michael A. Rebolledo ◽  
Joseph K. Perloff
Keyword(s):  
Arterial Aneurysm ◽  
Eisenmenger’S Syndrome ◽  
Pulmonary Arterial

scholarly journals Pulmonary arterial aneurysm presenting as an endobronchial mass.

Thorax ◽  
1995 ◽  
Vol 50 (9) ◽  
pp. 1013-1017 ◽  
Author(s):  
P M Gibbs ◽  
A Hami
Keyword(s):  
Arterial Aneurysm ◽  
Pulmonary Arterial

Chromosome 22q11 Deletion Complicated by Dissecting Pulmonary Arterial Aneurysm and Jejunal Atresia in an Infant

2000 ◽  
Vol 124 (6) ◽  
pp. 880-882
Author(s):  
Shoji Yamanaka ◽  
Yukichi Tanaka ◽  
Motoyoshi Kawataki ◽  
Rieko Ijiri ◽  
Kiyoshi Imaizumi ◽  
...  
Keyword(s):  
Digeorge Syndrome ◽  
Male Infant ◽  
Velocardiofacial Syndrome ◽  
Arterial Aneurysm ◽  
22Q11 Deletion ◽  
Jejunal Atresia ◽  
Chromosome 22Q11 ◽  
Apple Peel ◽  
Pulmonary Arterial ◽  
Arterial Aneurysms

Abstract We present an autopsy case of a 46-day-old male infant with chromosome 22q11 deletion, which is considered the primary cause of several diseases, including DiGeorge syndrome and velocardiofacial syndrome. The patient had 2 notable congenital abnormalities: multiple dissecting pulmonary arterial aneurysms distributed in both lungs and multiple jejunal atresia with apple-peel deformity. The former, a very rare pathologic condition especially in infancy, was found incidentally at autopsy and was the primary cause of death. To our knowledge, neither of these lesions has been reported previously in a patient with chromosome 22q11 deletion.

Levels of lipoprotein (a) in pulmonary arterial hypertension

2001 ◽  
Vol 11 (1) ◽  
pp. 25-29 ◽  
Author(s):  
Raul D. Santos ◽  
Antonio Foronda ◽  
José A. F. Ramires ◽  
Raul C. Maranhão
Keyword(s):  
Pulmonary Arterial Hypertension ◽  
Arterial Hypertension ◽  
Normal Population ◽  
Lipoprotein A ◽  
Eisenmenger’S Syndrome ◽  
Number Of Patients ◽  
Caucasian Patients ◽  
Pulmonary Arterial ◽  
Turbidimetric Assay ◽  
Genetically Determined

AbstractWe compared the levels of lipoprotein (a) in 48 Caucasian patients with pulmonary arterial hypertension, comprising 32 females and 16 males, aged 28.0 ± 12.0 years, with a range from 4 through 52 years, with 48 normal Caucasian subjects matched for age and sex. Pulmonary hypertension was secondary in 41 patients with Eisenmenger's syndrome, these comprising 27 females and 14 males aged 27.0 ± 12.0 years, with a range from 4 through 51 years, and primary in the other 7 patients, 5 females and 2 males, whose age was 30.0 ± 14.0 years, with a range from 9 through 52 years. Lipoprotein (a) was measured using an immunoprecipitation and turbidimetric assay after a 12 hour fast. Levels of the protein, expressed as the median (% 25; % 75), were higher in those with Eisenmenger's syndrome than in normal controls (p = 0.003). In addition, there was a greater prevalence of levels of lipoprotein greater than 30.0 mg/dl in those with secondary pulmonary arterial hypertension patients than in our normal population (p = 0.03). We have found no differences, however, in the levels of lipoprotein(a) in those who had primary pulmonary arterial hypertension when compared with their matched controls, albeit that the number of patients studied was small. We conclude that increased levels of lipoprotein (a) may be secondary to pulmonary arterial hypertension as a marker of tissue damage or may be genetically determined. In either way, the increase in lipoprotein (a) could be an additional factor predisposing to the vascular alterations known to occur in this disease.

Dissecting aneurysm of the pulmonary arteries—an unusual complication of congenital heart disease

1994 ◽  
Vol 4 (2) ◽  
pp. 131-135
Author(s):  
Thomas M. Farrell ◽  
Carol M. Cottrill ◽  
William N. O'Connor ◽  
Dede Boucher ◽  
Jacqueline A. Noonan
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Clinical Presentation ◽  
Surgical Intervention ◽  
Pulmonary Arteries ◽  
Dissecting Aneurysm ◽  
Unusual Complication ◽  
Arterial Aneurysm ◽  
Pulmonary Arterial

SummaryDissection of a pulmonary arterial aneurysm due to underlying pulmonary hypertension from congenital heart disease is uniformly fatal, but fortunately rare. Two such cases are presented, along with review of 24 other known cases published in the literature. Clinical presentation, guidelines tomanagement, and possible surgical intervention in the acutely dissecting patient are discussed.

scholarly journals Insidious Hughes Stovin Syndrome: Journey From Pulmonary Embolism to Pulmonary Arterial Aneurysm

2020 ◽  
Vol 21 (5) ◽  
pp. 350-353
Author(s):  
Merve Keskin ◽  
◽  
Gulru Polat ◽  
Aysu Ayranci ◽  
Gulistan Karadeniz ◽  
...  
Keyword(s):  
Pulmonary Embolism ◽  
Arterial Aneurysm ◽  
Pulmonary Arterial

scholarly journals Young onset hemoptysis: A rare cause of pulmonary arterial aneurysm

Lung India ◽  
2016 ◽  
Vol 33 (3) ◽  
pp. 345
Author(s):  
Akhil Paul ◽  
Yasir Peringattuthodiyil ◽  
DevasahayamJesudas Christopher ◽  
Balamugesh Thangakunam
Keyword(s):  
Arterial Aneurysm ◽  
Young Onset ◽  
Pulmonary Arterial

scholarly journals An unusual cause for fever of unknown origin: Pulmonary arterial aneurysm

2021 ◽  
Vol 36 (4) ◽  
pp. 620-622
Author(s):  
Samet Karahan ◽  
Şerife Emre ◽  
Zehra Beştepe Dursun
Keyword(s):  
Fever Of Unknown Origin ◽  
Unknown Origin ◽  
Arterial Aneurysm ◽  
Pulmonary Arterial

Dissecting pulmonary arterial aneurysm associated with chromosome 22q11 deletion

2001 ◽  
Vol 104 (3) ◽  
pp. 260-261 ◽  
Author(s):  
Yukichi Tanaka ◽  
Yoshikazu Kato ◽  
Keisuke Kato ◽  
Tetsumi Miyake ◽  
Rieko Ijiri ◽  
...  
Keyword(s):  
Arterial Aneurysm ◽  
22Q11 Deletion ◽  
Chromosome 22Q11 ◽  
Pulmonary Arterial
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