scholarly journals Double trouble: fetal diagnosis of a pulmonary artery sling and vascular ring

2016 ◽  
Vol 4 (12) ◽  
pp. 1187-1190 ◽  
Author(s):  
Jesse W. Lee ◽  
Beth F. Printz ◽  
Sanjeet R. Hegde ◽  
Lisa A. Vargas ◽  
Heather Y. Sun
PEDIATRICS ◽  
1982 ◽  
Vol 69 (4) ◽  
pp. 472-475
Author(s):  
Karen S. Rheuban ◽  
Nancy Ayres ◽  
J. Gordon Still ◽  
Bennett Alford

The pulmonary artery sling is a vascular anomaly that produces severe respiratory disease in infancy. The differential diagnosis is lengthy, and the diagnostic work-up frequently includes such invasive maneuvers as bronchography, bronchoscopy, and cardiac catheterization. In this paper the use of a new noninvasive diagnostic tool, computed tomography, to aid in the diagnosis of this form of vascular ring, is discussed and a review of salient features of this cardiovascular malformation is presented.


1970 ◽  
Vol 5 (3) ◽  
pp. 68-79
Author(s):  
Ana Carolina Melo ◽  
Barbara Costa Barros ◽  
Helena Sant’Anna Grilo

RESUMOIntrodução: Sling da artéria pulmonar, ou alça da artéria pulmonar é o nome que se dá a uma doença congênita, onde se forma um anel vascular incompleto que comprime estruturas importantes da região do mediastino. O quadro clínico pode ser desde assintomático podendo chegar ao óbito. Dos sintomáticos, mais da metade é diagnosticada logo nos primeiros meses de vida, porém nesses casos o quadro é geralmente leve e evolui de maneira lenta, porém progressiva. Estridor respiratório, tanto na inspiração quanto na expiração e cianose são sintomas comuns desses pacientes. Casuística: Esse projeto visa relatar um caso de Sling de artéria pulmonar, diagnosticado em um Hospital Escola do sul de Minas Gerais que se manifestou logo após o nascimento. Discussão: A criança em questão apresentou os sintomas clássicos da doença, porém devido sua raridade e variedade de diagnósticos diferenciais houve dificuldade em afirmar que se tratava de um Sling. Conclusão: Conclui-se que a doença foi diagnosticada e tratada a tempo e de maneira eficaz, embora fosse severa a gravidade do quadro apresentado pelo recém-nascido.Palavras-chave: Anel vascular, Sling de artéria pulmonar, Estridor respiratório. ABSTRACTIntroduction: Pulmonary artery sling or pulmonary artery handle is the name given to a congenital disease which forms an incomplete vascular ring that compresses important structures of the mediastinal region. The clinical picture may be from asymptomatic, experiencing mild cases turning to severe and even to death. More than half of symptomatic is diagnosed early in life, but in these cases the picture is generally mild and evolves slowly but progressively. Stridor, both in inspiration and in expiration and cyanosis are common symptoms of these patients. Case report: This project aims to report a case of pulmonary artery sling, diagnosed in a hospital school in southern Minas Gerais expressed just after birth. Discussion: The child presented classical symptoms of the disease, due to its rarity and another possible diagnosis was certain difficulty to be sure that it was a sling. Conclusion: The disease was diagnosed and treated on time and on the right way despite the severe gravity of the case presented by the newborn.Keywords: Vascular ring, Pulmonary artery sling, Stridor


2018 ◽  
Vol 28 (5) ◽  
pp. 783-785 ◽  
Author(s):  
Ziyad M. Binsalamah ◽  
Charles D. Fraser ◽  
Carlos M. Mery

AbstractPulmonary artery slings and vascular rings are very rare congenital anomalies. It is even rarer to have both anomalies in the same setting. We present a case of a toddler who was diagnosed with a left pulmonary artery sling and a vascular ring as part of the screening process for the VACTERL association – co-occurrence of vertebral, anorectal, cardiac, tracheoesophageal, renal, and limb malformations. He underwent a successful surgical repair via median sternotomy and on cardiopulmonary bypass with an uneventful postoperative course.


2014 ◽  
Vol 50 (8) ◽  
pp. 781-788 ◽  
Author(s):  
Benedetta Leonardi ◽  
Aurelio Secinaro ◽  
Renato Cutrera ◽  
Sonia Albanese ◽  
Marilena Trozzi ◽  
...  

2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Yoshimi Matsumoto ◽  
Masahiro Kamada ◽  
Naomi Nakagawa ◽  
Yukiko Ishiguchi

Abstract Background Double aortic arch (DAA) and pulmonary artery sling (PAS) are vascular ring formations that present in neonates and infants with symptoms of respiratory stenosis. Case summary The patient was a girl with suspected ventricular septal defect (VSD), right aortic arch (AA), left patent ductus arteriosus, and bilateral superior vena cava (SVC) on foetal echography in the first day of life. The girl was delivered at 40 weeks and 4 days of gestation. Ventricular septal defect, DAA, coarctation of the left AA, and bilateral SVC were diagnosed. Contrast-enhanced computed tomography at Day 16 revealed PAS with concurrent anomalous tracheal branching in addition to DAA. The right A2 segmental artery, which supplies the right upper pulmonary artery, showed abnormal branching from the left pulmonary artery (LPA). At 3 months of age, VSD patching, left AA resection distal to the root of the left subclavian artery, arterial ligament dissection, and LPA replacement were performed. Discussion Pulmonary artery sling coexists with anomalous branching of the trachea and abnormal branching of the right pulmonary artery (RPA). Our patient had an extremely rare case of DAA concurrent with PAS and presented with anomalous tracheal and RPA branching. We were concerned that increased pulmonary blood flow caused by the VSD would exacerbate tracheal displacement. Radical surgery at 3 months of age resulted in good postoperative progress.


2021 ◽  
pp. 1-9
Author(s):  
Putri Yubbu ◽  
Haifa Abdul Latiff ◽  
Husna Musa ◽  
Navin Kumar Devaraj ◽  
Nurul Adha Mohd Razif ◽  
...  

Abstract Background: Vascular compression of the airway often complicates CHD management. This study evaluated the use of CT in determining cardiovascular causes, clinical manifestations, and outcome of tracheobronchial compression among children with CHD. Methods: A retrospective review of clinical records of all patients with CT scan evidence of tracheobronchial compression from January 2007 to December 2017 at National Heart Institute. Cardiovascular causes of tracheobronchial compression were divided into three groups; group I: vascular ring/pulmonary artery sling, II: abnormally enlarged or malposition cardiovascular structure due to CHD, III: post-CHD surgery. Results: Vascular tracheobronchial compression was found in 81 out of 810 (10%) patients who underwent CT scan. Group I lesions were the leading causes of vascular tracheobronchial compression (55.5%), followed by group II (34.6%) and group III (9.9%). The median age of diagnosis in groups I, II, and III were 16.8 months, 3 months, and 15.6 months, respectively. Half of group I patients are manifested with stridor and one-third with recurrent chest infections. Persistent respiratory symptoms, lung atelectasis, or prolonged respiratory support requirement were clues in groups II and III. Higher morbidity and mortality in younger infants with severe obstructive airway symptoms, associated airway abnormalities, and underlying complex cyanotic CHD. Conclusions: Vascular ring/pulmonary artery sling and abnormally enlarged or malposition cardiovascular structure were the leading causes of cardiovascular airway compression. A high index of suspicion is needed for early detection due to its non-specific presentation. The outcome often depends on the severity of airway obstruction and complexity of cardiac lesions.


2018 ◽  
Vol 0 (1) ◽  
pp. 27-36
Author(s):  
D. Yu. Krivchenya ◽  
E. O. Rudenko

2021 ◽  
pp. 1-3
Author(s):  
Amna Al-Arnawoot ◽  
John Kavanagh ◽  
Elsie T. Nguyen

Abstract Bridging bronchi are the rarest of the major airway anomalies reported in the literature. In this brief report, we present a case of a symptomatic adult male patient presenting with a type 2 bridging bronchus associated with left pulmonary artery sling.


2020 ◽  
Vol 109 (1) ◽  
pp. e55-e57
Author(s):  
Marco Mammana ◽  
Andrea Zuin ◽  
Eugenio Serra ◽  
Alice Bellini ◽  
Federico Rea

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