Transcatheter aortic valve closure to treat severe aortic regurgitation in a patient failing stage I palliation for hypoplastic left heart syndrome

2009 ◽  
Vol 74 (6) ◽  
pp. 913-915 ◽  
Author(s):  
Frank-Thomas Riede ◽  
M. Kostelka ◽  
I. Dähnert
Keyword(s):  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Aortic Regurgitation ◽  
Valve Closure ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Severe Aortic Regurgitation ◽  
Transcatheter Aortic Valve ◽  
Aortic Valve Closure ◽  
Left Heart Syndrome

scholarly journals Prenatal Diagnosis and Successful Palliation of Absent Aortic Valve with Hypoplastic Left Heart Syndrome: A Case Report and Review of Literature

2019 ◽  
Vol 09 (02) ◽  
pp. e121-e126
Author(s):  
Amna Qasim ◽  
Chelsea Johnson ◽  
Muhammad Aly ◽  
Ashraf Aly
Keyword(s):  
Prenatal Diagnosis ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Main Pulmonary Artery ◽  
Aortic Insufficiency ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Aortic Valve Leaflets ◽  
Left Heart Syndrome

Introduction Congenital absence of the aortic valve leaflets is a rare association with hypoplastic left heart syndrome (HLHS). Case A 37-year-old pregnant woman was referred for fetal evaluation of possible HLHS at 22 weeks of gestation. The fetal echocardiogram (ECHO) was remarkable for a hypoplastic left atrium, nearly atretic mitral valve, small left ventricle, and a hypoplastic aortic valve with severe aortic insufficiency. A female infant was born at term and postnatal ECHO confirmed the above findings. In addition, there was complete absence of the aortic valve leaflets. The patient underwent Norwood's procedure at day 5 of life with atrial septectomy, over-sewing of the aortic valve annulus, and a 4 mm Sano's shunt between the right ventricle and the main pulmonary artery. She tolerated this surgery well and subsequently underwent a bidirectional Glenn's procedure at 8 months of life. Conclusion Prenatal diagnosis of absent aortic valve should be suspected in the presence of severe aortic insufficiency in the fetal ECHO. Early postnatal intervention is critical as those patients are likely to deteriorate quickly. The over-sewing of the aortic valve may be important to prevent coronary steal and myocardial hypoperfusion which could potentially be detrimental.

scholarly journals Improvement in right ventricular function by mitral valve closure in hypoplastic left heart syndrome

2021 ◽  
Author(s):  
Dai Asada ◽  
Yoko Kawai ◽  
Yoshinobu Maeda ◽  
Masaaki Yamagishi
Keyword(s):  
Mitral Valve ◽  
Right Ventricular ◽  
Ventricular Function ◽  
Hypoplastic Left Heart Syndrome ◽  
Right Ventricular Function ◽  
Left Ventricular ◽  
Valve Closure ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Abstract A male neonate presented with the aortic/mitral stenotic variant of hypoplastic left heart syndrome, wherein the suprasystemic left ventricular pressure and relatively large left ventricle had shifted the intraventricular septum. Despite bilateral pulmonary artery banding, the stroke volume was difficult to maintain owing to the compressed right ventricle, causing heart failure symptoms. Percutaneous balloon aortic valvuloplasty decreased the left ventricular pressure, restoring the right ventricular function. Norwood procedure with mitral valve closure after catheter intervention reduced the left ventricular size and improved the right ventricular function. This paper refers to the potential of mitral valve closure for hypoplastic left heart syndrome.

scholarly journals Fontan operation for hypoplastic left heart syndrome with absent aortic valve

2004 ◽  
Vol 128 (2) ◽  
pp. 315-316 ◽  
Author(s):  
Narutoshi Hibino ◽  
Yorikazu Harada ◽  
Takeshi Hiramatsu ◽  
Satoshi Yasukochi ◽  
Gengi Satomi
Keyword(s):  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Fontan Operation ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Absent Aortic Valve ◽  
Left Heart Syndrome

scholarly journals Comparison of Childhood Outcome by Mitral Valve and Aortic Valve Subtypes of Typical Hypoplastic Left Heart Syndrome

2018 ◽  
Vol 34 (1) ◽  
pp. 3-9
Author(s):  
Hirofumi Fukunaga ◽  
Makoto Nakamura ◽  
Shiro Ishikawa ◽  
Yoshihiko Kodama ◽  
Koichi Sagawa ◽  
...  
Keyword(s):  
Mitral Valve ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Mitral atresia with transposed great arteries and normal semilunar valves: a rare combination

2015 ◽  
Vol 26 (3) ◽  
pp. 599-601
Author(s):  
Gopalan Nair Rajesh ◽  
Sandeep Mohanan ◽  
Haridasan Vellani
Keyword(s):  
Blood Flow ◽  
Aortic Valve ◽  
Hypoplastic Left Heart Syndrome ◽  
Pulmonary Blood Flow ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Mitral Atresia ◽  
Rare Combination ◽  
Multiple Levels ◽  
Left Heart Syndrome

AbstractMitral atresia is commonly seen as a part of the spectrum of hypoplastic left heart syndrome, and it is usually associated with multiple levels of systemic outflow tract obstruction. Isolated mitral atresia with a normal aortic valve is extremely rare. We report the rare combination of mitral atresia, transposition of the great arteries, and unobstructed systemic and pulmonary blood flow.

First-Trimester Diagnosis of Hypoplastic Left Heart Syndrome: A Case Report

2021 ◽  
Vol 37 (2) ◽  
pp. 185-192
Author(s):  
Emily Hildebrand
Keyword(s):  
Case Report ◽  
Mitral Valve ◽  
Aortic Valve ◽  
Early Detection ◽  
Hypoplastic Left Heart Syndrome ◽  
First Trimester ◽  
Cardiac Anomaly ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Hypoplastic left heart syndrome (HLHS) comprises a spectrum of left-sided heart anomalies resulting from left outflow or inflow obstruction. Obstruction most often occurs at the levels of the aortic valve and/or mitral valve due to stenosis or atresia. HLHS is a lethal cardiac anomaly if not treated within the first week of life. Knowledge of sonographic features could aid in early detection, which results in better planning and management of pregnancy. This report presents a case in which HLHS was discovered during a routine dating and viability sonogram, performed at 12 weeks’ gestation.

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