scholarly journals The Pediatric Rheumatology European Society/American College of Rheumatology/European League against Rheumatism provisional classification criteria for juvenile systemic sclerosis

2007 ◽  
Vol 57 (2) ◽  
pp. 203-212 ◽  
Author(s):  
Francesco Zulian ◽  
Patricia Woo ◽  
Balu H. Athreya ◽  
Ronald M. Laxer ◽  
Thomas A. Medsger ◽  
...  
Keyword(s):  
Systemic Sclerosis ◽  
European Society ◽  
Pediatric Rheumatology ◽  
Classification Criteria ◽  
American College Of Rheumatology ◽  
European League Against Rheumatism ◽  
Juvenile Systemic Sclerosis ◽  
European League

Applying the ACR/EULAR Systemic Sclerosis Classification Criteria to the Spanish Scleroderma Registry Cohort

2015 ◽  
Vol 42 (12) ◽  
pp. 2327-2331 ◽  
Author(s):  
Luis Sáez-Comet ◽  
Carmen Pilar Simeón-Aznar ◽  
Mercedes Pérez-Conesa ◽  
Carmen Vallejo-Rodríguez ◽  
Carles Tolosa-Vilella ◽  
...  
Keyword(s):  
Systemic Sclerosis ◽  
Multicenter Study ◽  
Classification Criteria ◽  
Raynaud Phenomenon ◽  
Cross Sectional ◽  
American College Of Rheumatology ◽  
European League Against Rheumatism ◽  
European League

Objective.To compare American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) classification criteria for systemic sclerosis (SSc) with previous American Rheumatology Association (ARA) criteria.Methods.This was a cross-sectional multicenter study comparing sensitivity of both criteria in the cutaneous subsets in the Spanish scleroderma registry (RESCLE) cohort.Results.In 1222 patients with SSc, the most prevalent items were Raynaud phenomenon (95%), skin thickening (91%), and abnormal capillaroscopy (89%). ARA criteria classified as SSc 63.5% of all patients, and 63%, 100%, 11.2%, and 0% in the limited, diffuse, sine, and pre-SSc subsets, respectively. ACR/EULAR criteria classified 87.5% of all patients and 98.5%, 100%, 41.8%, and 15.9% in the same subsets, respectively.Conclusion.ACR/EULAR criteria are more sensitive than ARA criteria, especially in limited, sine, and pre-SSc subsets.

Performance of the 2013 American College of Rheumatology/European League Against Rheumatism Classification Criteria for Systemic Sclerosis (SSc) in Large, Well-defined Cohorts of SSc and Mixed Connective Tissue Disease

2014 ◽  
Vol 42 (1) ◽  
pp. 60-63 ◽  
Author(s):  
Anna-Maria Hoffmann-Vold ◽  
Ragnar Gunnarsson ◽  
Torhild Garen ◽  
Øyvind Midtvedt ◽  
Øyvind Molberg
Keyword(s):  
Systemic Sclerosis ◽  
Connective Tissue ◽  
Connective Tissue Disease ◽  
Mixed Connective Tissue Disease ◽  
Classification Criteria ◽  
University Hospital ◽  
American College Of Rheumatology ◽  
European League Against Rheumatism ◽  
Item Data ◽  
European League

Objective.To assess the 2013 American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) Classification Criteria for Systemic Sclerosis (SSc) on defined subgroups of SSc and in mixed connective tissue disease (MCTD) as an SSc-related disease.Methods.The 2013 ACR/EULAR criteria were assessed in 425 consecutive patients suspected to have SSc and seen at Oslo University Hospital, and in the nationwide Norwegian MCTD cohort (n = 178). In the SSc group, 239/425 patients had disease duration < 3 years (in 82 of these, duration was < 1 yr). Patients were subgrouped as limited SSc (n = 294), diffuse SSc (n = 97), SSc sine scleroderma (n = 10), and early SSc (prescleroderma; n = 24). Item data were complete, except nailfold capillaroscopy and telangiectasia results, missing in the MCTD cohort.Results.The 2013 ACR/EULAR SSc criteria were met by 409/425 patients (96%) in the SSc group. For comparison, only 75% (293/391) met the 1980 ACR SSc classification criteria. All the novel items in the 2013 ACR/EULAR criteria were frequent in the SSc cohort. Considering that there were missing data on 2 items, 10% (18/178) of the MCTD cohort met the 2013 ACR/EULAR criteria, giving an estimated specificity of 90% toward this SSc-like disorder.Conclusion.In our large and representative group of consecutive patients with SSc, the 2013 ACR/EULAR SSc criteria were more sensitive than the ACR 1980 criteria. However, the new criteria did not completely segregate SSc from MCTD, making specificity a potential issue.

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