scholarly journals Death during an asthma exacerbation in an adult with sickle cell disease: An autopsy case study

2013 ◽  
Vol 88 (9) ◽  
pp. 824-824 ◽  
Author(s):  
Binod Dhakal ◽  
Kristinza Giese ◽  
Linus Santo-Thomas ◽  
Joshua J. Field
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Asthma Exacerbation ◽  
Autopsy Case ◽  
Cell Disease

scholarly journals Accelerated approval of Oxbryta® (voxelotor): A case study on novel endpoint selection in sickle cell disease

2020 ◽  
Vol 98 ◽  
pp. 106161
Author(s):  
Joshua Lehrer-Graiwer ◽  
Linda Yokoshima ◽  
Barbara Tong ◽  
Ted W. Love
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Cell Disease ◽  
Accelerated Approval

Nifedipine Increases Cerebral Blood Flow in Sickle Cell Disease: A Case Study

1994 ◽  
Vol 9 (3) ◽  
pp. 337-338 ◽  
Author(s):  
Stephen Ashwal ◽  
Antranik Bedros ◽  
Joseph Thompson
Keyword(s):  
Blood Flow ◽  
Cerebral Blood Flow ◽  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Cell Disease

scholarly journals VP194 Health Technology Assessment Applied To Nurse Retention And Development: A Sickle Cell Example

2017 ◽  
Vol 33 (S1) ◽  
pp. 239-239
Author(s):  
Julia Lavenberg ◽  
Matthew Mitchell ◽  
Kendal Williams ◽  
Craig Umscheid
Keyword(s):  
Job Satisfaction ◽  
Sickle Cell Disease ◽  
Communication Skills ◽  
Sickle Cell ◽  
Support Group ◽  
Education Program ◽  
Nurse Retention ◽  
Health Technology ◽  
Cell Disease

INTRODUCTION:Health Technology Assessment (HTA) methods are usually applied to the evaluation of drugs, devices, and procedures. We have used HTA to promote evidence-based decision-making on topics relating to staffing and career development for healthcare professionals. Interventions to reduce the stress associated with caring for patients who need repeated hospitalization such as patients with sickle cell disease are thought to improve job satisfaction and nurse retention, but is there scientific evidence to support them?METHODS:We systematically searched Medline, CINAHL, PsycINFO, Cochrane, and Joanna Briggs Institute databases for published studies evaluating interventions targeting healthcare personnel. Searches combined tems for sickle cell disease with terms for job stress, turnover, and other career-related outcomes. We evaluated the quality of individual studies using standardized checklists and constructed evidence tables.RESULTS:We found one randomized trial (RCT) of an education program for nurses and physicians, a pre-post analysis of a communication skills and cultural awareness program, and a case study of a nurse support group. The RCT found that an education program significantly improved participants attitude towards patients but did not measure any outcomes relating to caregiver stress or job satisfaction. The pre-post study found that a communication skills program significantly improved nurses confidence in their ability to communicate with patients. The case study reported that nurses found the support group useful and felt their attitudes were improved, but there was no control group to compare their responses to. The education program was graded as moderate-strength evidence and the other programs had low-strength evidence. There was no meta-analysis or other data synthesis of the results because of the differing interventions and outcome measures.CONCLUSIONS:There have been few quantitative scientific evaluations of the effectiveness of interventions to reduce the stress nurses feel when caring for sickle cell disease patient. The studies that have been published have favorable conclusions towards these interventions, but the strength of evidence is not high.

scholarly journals Family management ofchildren who experience sickle cell disease: a qualitative study

2020 ◽  
Vol 73 (suppl 4) ◽  
Author(s):  
Elaine Cristina Rodrigues Gesteira ◽  
Regina Szylit ◽  
Maiara Rodrigues dos Santos ◽  
Carolliny Rossi de FariaIchikawa ◽  
Patricia Peres de Oliveira ◽  
...  
Keyword(s):  
Sickle Cell Disease ◽  
Sickle Cell ◽  
Management Style ◽  
Family Management ◽  
Management Styles ◽  
Cell Disease ◽  
Structured Interviews ◽  
The Family ◽  
Nurses Role

ABSTRACT Objective: to know the family management experience of children with sickle cell disease in the light of the Family Management Style Framework. Methods: a qualitative case study carried out between September/2015 and July/2016 with 12 members of eight families registered in a blood center in Minas Gerais. The semi-structured interviews were recorded, and the data were analyzed and interpreted by the hybrid model thematic analysis. Results: three management styles were identified: five families in the accommodating style; two families in the struggling style; and only one family in the enduring style.It was noted that empowerment was paramount in the acquisition of skills and abilities to care for these children. Final considerations: family management knowledge of children with sickle cell disease provided a reflection on nurses’ role in supporting, orienting and encouraging the empowerment of these families aiming at the search for comprehensive care.

Sickle Cell Disease and Hidden Hearing Loss

2020 ◽  
pp. 180-194
Author(s):  
Diane M. Scott
Keyword(s):  
United States ◽  
Hearing Loss ◽  
Sickle Cell Disease ◽  
Sickle Cell ◽  
The United States ◽  
Cell Disease ◽  
Hearing Thresholds ◽  
Hidden Hearing Loss

Sickle cell disease (SCD) is an autosomal recessively inherited group of red blood cell disorders. It is more commonly found in African Americans and Hispanics in the United States. The sickle-shaped cells characteristic of the disease cause physiological problems, including hemolytic anemia and vaso-occlusion. Research has linked hearing loss to sickle cell disease. Studies have shown that children and adults with sickle cell disease may have higher rates of sensorineural and central auditory hearing impairment. This case study examines hidden hearing loss in an African American boy with SCD who presents with normal hearing thresholds. It also discusses the role of audiologists in the care of individuals with sickle cell disease and hearing loss.

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