Multiple Skin-Colored Papules With Diffuse Sclerosis

2014 ◽  
Vol 150 (8) ◽  
pp. 893
Author(s):  
Danielle S. Applebaum ◽  
Seema Daulat ◽  
Madeleine Duvic
Keyword(s):  
Diffuse Sclerosis

Diffuse Sclerosis

2015 ◽  
pp. 177-180
Author(s):  
Diya F. Mutasim
Keyword(s):  
Diffuse Sclerosis

Diffuse Sclerosis with Preserved Myelin Islands: A Pathological Report of a Case, with a Note on Cerebral Involvement in Raynaud's Disease

1939 ◽  
Vol 85 (354) ◽  
pp. 22-28 ◽  
Author(s):  
B. Horanyi-Hechst ◽  
A. Meyer
Keyword(s):  
Rapid Progression ◽  
Spastic Paraplegia ◽  
Clinical Symptomatology ◽  
Slowing Down ◽  
Familial Form ◽  
Intercurrent Disease ◽  
The One ◽  
Pathological Report ◽  
Disseminated Sclerosis ◽  
Diffuse Sclerosis

Pelizaeus (1885) described a family of which five members exhibited a rather uniform clinical symptomatology, consisting of tremor of the head, nystagmus, spastic paraplegia, etc. He thought he was dealing with an atypical familial form of disseminated sclerosis. Twenty-five years later Merzbacher (1910) investigated the same family and found the symptoms in twelve members, representing four generations. Symptomatology and clinical course of the condition was, in all patients, approximately identical: onset within the first months of life, rapid progression within the first six years, slowing down later considerably, death after twenty to thirty years due to intercurrent disease. The symptoms were tremor of the head, nystagmus; later paraplegia, ataxia, visual and auditory disturbances, involuntary movements, etc. The emotional and intellectual sphere remained comparatively unimpaired. The heredity was found to be recessive: the mothers, though themselves spared by the disease, pass it on to their sons (though among the twelve cases of Merzbacher there were also two females). In the one case investigated histopathologically by Merzbacher a diffuse demyelinization was found, particularly marked within the occipital region, distributed symmetrically in both the hemispheres and characterized by the persistence of myelin islands, often around vessels, which gave the condition the appearance of a tiger's skin. Merzbacher thought he was dealing with an hereditary aplasia of axis cylinders and myelin fibres, and called the condition aplasia axialis extra-corticalis congenita.

Diffuse sclerosis with adrenal insufficiency

Neurology ◽  
1968 ◽  
Vol 18 (11) ◽  
pp. 1066-1074 ◽  
Author(s):  
N. A. Vick ◽  
R. Y. Moore
Keyword(s):  
Adrenal Insufficiency ◽  
Diffuse Sclerosis

scholarly journals Devic's neuromyelitis optica and Schilder's myelinoclastic diffuse sclerosis

1992 ◽  
Vol 55 (12) ◽  
pp. 1194-1196 ◽  
Author(s):  
J A Hainfellner ◽  
M Schmidbauer ◽  
E Schmutzhard ◽  
H Maier ◽  
H Budka
Keyword(s):  
Neuromyelitis Optica ◽  
Devic’S Neuromyelitis Optica ◽  
Diffuse Sclerosis

Decompressive aspiration in myelinoclastic diffuse sclerosis or Schilder disease

2002 ◽  
Vol 97 (6) ◽  
pp. 1447-1449 ◽  
Author(s):  
Farideh Nejat ◽  
Behzad Eftekhar
Keyword(s):  
White Matter ◽  
Intracranial Hypertension ◽  
Demyelinating Disease ◽  
Corticosteroid Treatment ◽  
Mass Effect ◽  
Subcortical White Matter ◽  
Brain Images ◽  
Content Type ◽  
Fine Print ◽  
Diffuse Sclerosis

✓ This 9-year-old girl with rapidly progressive cerebral demyelinating disease presented with hemiplegia and intracranial hypertension. Brain images revealed four lesions with mass effect in the subcortical white matter of both hemispheres. Demyelination was found on pathological studies of these lesions. The patient experienced some recovery with corticosteroid treatment but improved completely with decompressive aspiration of the largest lesion.

Simultaneous Diffuse Sclerosis Variant of Papillary Thyroid Carcinoma and Diffuse Toxic Hyperplasia (Graves' Disease)

2004 ◽  
Vol 15 (1) ◽  
pp. 77-82 ◽  
Author(s):  
Gladell P. Paner ◽  
Jennifer L. Hunt ◽  
Marlyn C. Ciesla ◽  
Steven DeJong ◽  
Virginia LiVolsi
Keyword(s):  
Papillary Thyroid Carcinoma ◽  
Thyroid Carcinoma ◽  
Graves Disease ◽  
Papillary Thyroid ◽  
Diffuse Sclerosis
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